Anesthetic management in Joubert syndrome.
VODOPICH, DARKO J. MD; GORDON, GREGORY J. MD
[Report] Pediatric Anesthesia. 14(10):871-873, October 2004.

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Summary: We review the anesthetic implications of Joubert syndrome and report that spinal anesthesia under intravenous propofol sedation proved satisfactory for repair of an inguinal hernia in a spontaneously ventilating infant with this syndrome. We caution that anatomical peculiarities may complicate performance of a caudal epidural block and suggest consideration of the use of caffeine to ameliorate the apneic episodes seen in early infancy in this syndrome.

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